Congenital epidermolysis bullosa: practical aspects of comprehensive treatment
DOI:
https://doi.org/10.15574/SP.2024.7(143).116121Keywords:
congenital epidermolysis bullosa, newborn baby, multidisciplinary approach, clinical caseAbstract
Epidermolysis bullosa is a chronic illness with early manifestations. Disease currently does not have specific treatment and is characteristic of high disability rate outcomes which implies significant impact on life quality.
Aim - considered clinical case discusses early prophylaxis of unfavorable outcomes with disability and rationale for multidisciplinary approach to care and management BE patients.
Discussed clinical case evaluates using combustiology based approaches and techniques to treatment of early stages of illness, discusses pain intensity estimation and management, indications for antibacterial therapy, nutritional demands and skin care aspects from multidisciplinary standpoints.
Conclusions. Using combustiology based approaches for estimation of severity and area skin injuries and plastic surgery techniques for severe types of EB in newborn period may prevent early development of disability. Multidisciplinary approach since birth gives opportunity to provide comprehensive treatment, define follow-up strategy and family support.
The study was carried out in accordance with the main provisions of the Declaration of Helsinki. The consent of the child's parents was obtained for the study.
The authors declare no conflict of interest.
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